Klippel-Trenaunay Sendromunda Alt Gastrointestinal Kanama, Mesane ve Dalakta Hemanjiomlar: Nadir Görülen Olgu Sunumu
Küçük Resim Yok
Tarih
2022
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Bolu Abant İzzet Baysal Üniversitesi
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Klippel-Trenaunay Sendromu (KTS); genellikle doğumda veya erken bebeklik döneminde ortaya çıkan kütanöz hemanjiyom, doğuştan venöz anomaliler, kemik ve yumuşak dokuda hipertrofi ile karakterizedir. Çoğunlukla periferik bulgularla tanı alan KTS nadirde olsa gastrointestinal sistemi (GİS) içeren vasküler malformasyonlar ile birlikte de karşımıza çıkabilir. Bu yazıda rektal kanama ve anemi şikayeti ile başvuran, herhangi bir periferik bulgusu olmadan distal kolon, rektum, mesane ve dalak tutulumuyla karşımıza çıkan 45 yaşında erkek hasta sunulmuştur. Anemi tedavisi ve transfüzyona yanıt alınamayan hastada küratif tedavi olarak rektosigmoid rezeksiyon (low-anterior rezeksiyon) ve kolorektal anastomoz ameliyatı uygulandı.
Klippel-Trenaunay Syndrome (KTS); It is characterized by cutaneous hemangioma, congenital venous anomalies, bone and soft tissue hypertrophy usually occurring at birth or in early infancy. KTS, which is mostly diagnosed with peripheral findings, can rarely be encountered with vascular malformations involving the gastrointestinal system (GIS). We herein report a 45-year-old male patient who admitted with rectal bleeding and anemia and presented with distal colon, rectum, bladder and spleen involvement without any peripheral findings. Rectosigmoid resection (low-anterior resection) and colorectal anastomosis surgery were performed as curative treatment in the patient who did not respond to anemia treatment and transfusion.
Klippel-Trenaunay Syndrome (KTS); It is characterized by cutaneous hemangioma, congenital venous anomalies, bone and soft tissue hypertrophy usually occurring at birth or in early infancy. KTS, which is mostly diagnosed with peripheral findings, can rarely be encountered with vascular malformations involving the gastrointestinal system (GIS). We herein report a 45-year-old male patient who admitted with rectal bleeding and anemia and presented with distal colon, rectum, bladder and spleen involvement without any peripheral findings. Rectosigmoid resection (low-anterior resection) and colorectal anastomosis surgery were performed as curative treatment in the patient who did not respond to anemia treatment and transfusion.
Açıklama
Anahtar Kelimeler
Klippel-Trenaunay Sendromu|Gastrointestinal Kanama|Hemanjiyom|Klippel Trenaunay Syndrome|Gastrointestinal Bleeding|Hemangioma
Kaynak
Abant Medical Journal
WoS Q Değeri
Scopus Q Değeri
Cilt
11
Sayı
3
